Alagille Syndrome: A case report of a rare oral and multisystem manifestation

Alagille syndrome is an inherited multisystem disorder of autosomal dominant transmission. Its prevalence estimated at 1 per 70,000 to 100,000 live births. We report the case a young patient suffering from who consulted center diagnosis and dental treatment Rabat - MOROCCO (CCTD). The general manifestations are facial dysmorphia, hepatic, cardiac, ocular disorders. Hepatic cholestasis causes oral repercussions such as yellow mucosa, hypomineralization teeth, high tendency caries. management requires knowledge health patient, therefore collaboration with attending physicians, establishment rigorous hygiene, personalized prophylaxis consequent contribution fluorine.